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Sirenomelia reporte de un caso / Sirenomelia: a case report
Resumen
Resumen
La sirenomelia es una anomalía congénita rara, caracterizada por la fusión de las extremidades inferiores y múltiples anormalidades viscerales. Habitualmente tiene un pronóstico letal por la gravedad de las anormalidades asociadas. En este trabajo se presenta el caso de una paciente de 26 años, secundigesta y sin comorbilidades asociadas, que ingresó al servicio de Urgencias por un embarazo de 26 semanas y anhidramnios, posteriormente se le realizó un ultrasonido en el servicio de Medicina Materno Fetal en donde se realizó el diagnóstico de sirenomelia. Se decidió la interrupción del embarazo por el mal pronóstico.
Abstract
Sirenomelia is a rare congenital anomaly characterized by fusion of the lower extremities and multiple visceral abnormalities. It usually has a lethal prognosis due to the severity of the associated abnormalities. We present the case of a 26-year-old female patient, in her second pregnancy without associated comorbidities, who was admitted to the Emergency department due to a 26-week pregnancy and anhydramnios. She subsequently underwent an ultrasound in the Maternal Fetal Medicine service, who performed the Sirenomelia diagnosis. It was decided to terminate the pregnancy due to the poor prognosis.
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DOI: https://doi.org/10.24875/10.5281/zenodo.13306810
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