Las anomalías de los ductos müllerianos o paramesonéfricos son un conjunto de malformaciones congénitas del tracto genital femenino que resultan de la alteración en una o más fases del desarrollo embriológico. La prevalencia ha incrementado, probablemente debido al progreso de los métodos diagnósticos de imagen y a la relevancia que han adquirido en mujeres jóvenes con problemas de infertilidad. Actualmente la resonancia magnética es el método de elección para caracterizar los diferentes tipos de anomalías müllerianas, sus complicaciones y la patología asociada. El útero unicorne corresponde a la clase II de la clasificación de anomalías de los ductos müllerianos desarrollada por la Sociedad Americana de Medicina Reproductiva. Según esta, se identifican cuatro subtipos, cada uno con diferente implicación clínica. El útero unicorne con cuerno uterino rudimentario cavitado no comunicante está asociado con una incidencia incrementada de problemas ginecológicos y complicaciones obstétricas que en ocasiones amenazan la vida de las pacientes, razón por la que es necesaria su sospecha, diagnóstico y tratamiento oportunos. Presentamos el caso de una paciente con problemas de infertilidad en la que se descubrió este subtipo de malformación congénita.
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