Type I Chiari malformation associated with cerebellar atrophy. Case Report
Main Article Content
Keywords
Arnold-Chiari malformation, Laminectomy, Neural tube defects
Abstract
Chiari malformation is characterized by caudal displacement of the cerebellar tonsils that penetrate into the spinal canal through the foramen magnum, achieving reach the atlas or axis. trunk and any drop of the fourth ventricle is observed. Typically is seen in young adults. In some cases scoliosis and Syringomyelic cavities may occur. The authors present (as far as they know) the first case in the literature with long term follow-up, of a caucasian woman with an unusual form of cerebellar atrophy and Chiari Type I malformation, suffering from weakness in his upper and lower extremities with rapidly progression. The patient was successfully treated with suboccipital decompression and C1 laminectomy.
References
Anson J, Benzel E, Awad I. Syringomyelia and the Chiari malformations. Park Ridge, Illinois: American Association of Neurological Surgeons; 1997. pp. 91-104.
Haroun RI, Guarnieri M, Meadow JJ, Kraut M, Carson BS. Current opinions for the treatment of syringomyelia and chiari malformations: Survey of the Pediatric Section of the American Association of Neurological Surgeons. Pediatr Neurosurg . 2000;33(6):311-7.
Meadows J, Kraut M, Guarnieri M, Haroun RI, Carson BS. Asymptomatic Chiari Type I malformations identified on magnetic resonance imaging. J Neurosurg . 2000;92(6):920-6.
Furtado SV, Reddy K, Hegde AS. Posterior fossa morphometry in symptomatic pediatric and adult Chiari I malformation. J Clin Neurosci . 2009;16(11):1449-54.
Gebarski SS, Greenberg HS. Chiari malformation presenting as loss of cerebellar substance on computed tomography. Surg Neurol. 1984;21(6):562-4.
Naidich TP, Pudlowski RM, Naidich JB. CT signs of Chiari malformations. Part I, II and III. Radiology. 1980;134:65-71, 391-8, 657-63.
Elliott NSJ, Bertram CD, Martin BA, Brodbelt AR. Syringomyelia: A review of the biomechanics. J Fluids Struct . 2013;40:1-24.
Oldfield EH, Muraszko K, Shawker TH, Patronas NJ. Pathophysiology of syringomyelia associated with Chiari I malformation of the cerebellar tonsils. Implications for diagnosis and treatment. J Neurosurg . 1994;80(1):3-15
Lee HS, Lee S-H, Kim ES, Kim J-S, Lee J-I, Shin HJ, et al. Surgical results of arachnoid-preserving posterior fossa decompression for Chiari I malformation with associated syringomyelia. J Clin Neurosci. 2012;19(4):557-60.
Yilmaz A, Kanat A, Musluman AM, Çolak İ, Terzi Y, Kayacı S, et al. When is duraplasty required in the surgical treatment of Chiari malformation Type I based on tonsillar descending grading scale? World Neurosurg . 2011;75(2):307-13.
Kalb S, Perez-Orribo L, Mahan M, Theodore N, Nakaji P, Bristol RE. Evaluation of operative procedures for symptomatic outcome after decompression surgery for Chiari type I malformation. J Clin Neurosci. 2012;19(9):1268-72.