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Low-grade fibromyxoid sarcoma with pulmonary metastasis. A rare case report

Authors

  • Hugo Eduardo Morales-De Fuentes <p>Instituto Mexicano del Seguro Social, Centro M&eacute;dico Nacional Siglo XXI, Hospital de Oncolog&iacute;a, Servicio de Tumores de T&oacute;rax. Ciudad de M&eacute;xico</p> http://orcid.org/0000-0002-9452-4934
  • María Fernanda Monraz-Méndez <p>Instituto Mexicano del Seguro Social, Centro M&eacute;dico Nacional Siglo XXI, Hospital de Oncolog&iacute;a, Servicio de Tumores de T&oacute;rax. Ciudad de M&eacute;xico</p> http://orcid.org/0000-0003-4625-0403

Keywords:

Sarcoma, Lung Neoplasms, Neoplasm Metastasis

Abstract

Background: Low-grade fibromyxoid sarcoma is a very rare tumor that tends to develop in deep soft tissues of young adults and has the potential for local recurrence and distant metastasis.

Clinical case: We present the case of a 36-year-old man with a low-grade fibromyxoid sarcoma in the right shoulder, which was initially reported as a 4-year-old tumor, undergoing extensive resection with a histopathological report of low-grade fibromyxoid sarcoma, whose deep surgical edge was in bony contact. A simple and contrasted axial tomography was performed where an 8 mm left lung lesion was observed in the upper lobe lower lingular segment of heterogeneous content, hyperdense with contrast medium reinforcement. Left lateral thoracotomy is performed for metastasectomy and pathology corroborates the diagnosis of metastasis from fibromyxoid sarcoma.

Conclusion: Low histological fibromyxoid sarcoma is a very rare tumor that must be differentiated from other soft tissue tumors. Recurrences and metastases are reported, despite short or prolonged disease-free periods of up to 50 years, so patients with a history of this tumor should be followed up.

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Author Biographies

  • Hugo Eduardo Morales-De Fuentes, <p>Instituto Mexicano del Seguro Social, Centro M&eacute;dico Nacional Siglo XXI, Hospital de Oncolog&iacute;a, Servicio de Tumores de T&oacute;rax. Ciudad de M&eacute;xico</p>

    Egresado de la licenciatura en Médico Cirujano de la Universidad Anáhuac México Norte con un promedio de 91.2. Actualmente Residente de segundo año de cirugía general del Instituto Mexicano del Seguro Social con sede en Centro Médico Nacional Siglo XXI.  

  • María Fernanda Monraz-Méndez, <p>Instituto Mexicano del Seguro Social, Centro M&eacute;dico Nacional Siglo XXI, Hospital de Oncolog&iacute;a, Servicio de Tumores de T&oacute;rax. Ciudad de M&eacute;xico</p>

    Residente de tercer año de cirugía general del Instituto Mexicano del Seguro Social con sede en Centro Médico "Ignacio García Téllez" T1 Mérida, Yucatán.

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Published

2020-04-13

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Issue

Vol. 58 No. 2 (2020): March-April

Section

Clinical Cases

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