Perforated metastatic primary fibromyxoid sarcoma of the transverse colon
Main Article Content
Keywords
Intestinal Perforation, Neoplasm Metastasis, Colonic Neoplasms
Abstract
Background: Low grade fibromyxoid sarcoma (LGFMS) is considered a rare soft tissue tumor and has a tendency to arise from deep soft tissue of the trunk and lower extremities, the intraabdominal area is considered a rare location.
Objective: To describe the first case of a LGFMS arising from the transverse colon with liver metastasis.
Clinical case: We describe a 57-years-old male patient with abdominal pain of sudden onset; at surgery he was found to have an abscessed tumor in the transverse colon that infiltrated to mesentery root. An extended left hemicolectomy was performed with ascending colon colostomy. Later on, a postoperative scan he was found to have metastatic liver disease.
Conclusions: This case is unique in terms of the location and presentation. It’s a reminder of differential diagnosis of acute abdominal pain. To our knowledge is the first case of a LGFMS of the colon with synchronous liver metastasis.
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